Input interpretation
![heme biosynthesis from uroporphyrinogen I (human metabolic pathway)](../image_source/7a8860e49afd615b4c059d2cf3ba9dab.png)
heme biosynthesis from uroporphyrinogen I (human metabolic pathway)
Pathway topology
![Pathway topology](../image_source/dea7e5f8d8725152cfbd55806e0e5430.png)
Pathway topology
Pathway components
![| uroporphyrinogen-III | 836.8 g/mol | | C_40H_40N_4O_16 | coproporphyrinogen III | coproporphyrinogen | 660.8 g/mol | | C_36H_40N_4O_8 | protoporphyrinogen IX | protoporphyrinogen | 568.7 g/mol | | C_34H_36N_4O_4 | protoporphyrin IX | 566.7 g/mol | | C_34H_33N_4O_4 | heme | 616.5 g/mol | | C_34H_32FeN_4O_4](../image_source/b40f7f83c4c6bf54f8795a1a19719b9e.png)
| uroporphyrinogen-III | 836.8 g/mol | | C_40H_40N_4O_16 | coproporphyrinogen III | coproporphyrinogen | 660.8 g/mol | | C_36H_40N_4O_8 | protoporphyrinogen IX | protoporphyrinogen | 568.7 g/mol | | C_34H_36N_4O_4 | protoporphyrin IX | 566.7 g/mol | | C_34H_33N_4O_4 | heme | 616.5 g/mol | | C_34H_32FeN_4O_4
Pathway steps
![| reaction ⟶ | ⟶ + CO_2 | uroporphyrinogen decarboxylase ⟶ | + oxygen + H+ ⟶ + CO_2 + H_2O | coproporphyrinogen III oxidase, mitochondrial precursor ⟶ | + oxygen ⟶ + H_2 | protoporphyrinogen oxidase ⟶ | + Fe_2+ ⟶ + H+ | ferrochelatase, mitochondrial precursor](../image_source/d282a9232b08ffe04883b61a10257541.png)
| reaction ⟶ | ⟶ + CO_2 | uroporphyrinogen decarboxylase ⟶ | + oxygen + H+ ⟶ + CO_2 + H_2O | coproporphyrinogen III oxidase, mitochondrial precursor ⟶ | + oxygen ⟶ + H_2 | protoporphyrinogen oxidase ⟶ | + Fe_2+ ⟶ + H+ | ferrochelatase, mitochondrial precursor
Related pathways
![| overlapping components tetrapyrrole biosynthesis II | tetrapyrrole biosynthesis I |](../image_source/b50823aabd22e34ccfefed9d39f63aac.png)
| overlapping components tetrapyrrole biosynthesis II | tetrapyrrole biosynthesis I |